Inclusions, sickling screens, erythrocytosis and the ESR
15 min
- Choose an iron stain to confirm suspected Pappenheimer bodies
- Report a positive Hb S solubility screen without calling trait or disease
- Choose between a repeat count, EPO, and JAK2 V617F for a raised hemoglobin
- Recognize how citrate ratio, anemia, tube tilt, and temperature change a Westergren ESR
Try first
Get the idea
Confirm iron before you report it
Pappenheimer bodies, Howell-Jolly bodies, and basophilic stippling can all look dark on a Wright-stained film. Only Pappenheimer bodies contain iron, and a Prussian blue stain is what confirms it.1 Reporting iron granules without that stain can mistake another inclusion for the iron-loaded cells of sideroblastic anemia, so a suspicious clustered granule pattern is stained before it is named.
A positive screen goes on to fractionation
A positive Hb S solubility screen shows that a sickling hemoglobin is present in some amount. Trait and sickle cell disease both give a positive result, so the screen alone cannot separate them, and every positive result goes on to electrophoresis or high-performance liquid chromatography (HPLC).2,3 A negative screen does not exclude a sickling hemoglobin either, in severe anemia, in a young infant with a large Hb F fraction, or after recent transfusion.2
Confirm persistence before you test genes
A raised hemoglobin is confirmed against prior results before anything else is ordered, because plasma-volume loss, hypoxia, and other causes can raise it without a true increase in red-cell mass.4 Serum erythropoietin (EPO) comes next: a subnormal result supports a primary process, and a normal or increased result supports a secondary cause. JAK2 V617F is tested when polycythemia vera is plausible, and skipping the EPO step sends a plausible secondary cause straight to molecular testing it may not need.4
The tube and the technique change the ESR
The Westergren reference method needs blood diluted 4:1 with citrate or saline. An ordinary coagulation tube carries the wrong 9:1 ratio for this method.5 Anemia raises the result on its own, without any change in inflammation, and a tilted tube, vibration, or high temperature raises it further.5,6 Read every ESR with the hematocrit.
References
- Keohane EM, Preston MM, Mirza KM, Walenga JM, eds. Rodak's Hematology: Clinical Principles and Applications. 7th ed. Elsevier; 2025. Accessed September 26, 2026. https://www.us.elsevierhealth.com/rodaks-hematology-9780323936507.html
- Mayo Clinic Laboratories. Sickle solubility, blood (SDEX). Clinical Information, Cautions, and Method Description. Accessed September 26, 2026. https://www.mayocliniclabs.com/test-catalog/Overview/9180
- Bender MA, Carlberg K. Sickle cell disease. In: Adam MP, Bick S, Mirzaa GM, et al, eds. GeneReviews. University of Washington, Seattle; 2003. Revised February 13, 2025. Accessed September 26, 2026. https://www.ncbi.nlm.nih.gov/books/NBK1377/
- Noumani I, Harrison CN, McMullin MF. Erythrocytosis: diagnosis and investigation. Int J Lab Hematol. 2024;46(suppl 1):55-62. doi:10.1111/ijlh.14298
- Jou JM, Lewis SM, Briggs C, Lee S-H, De La Salle B, McFadden S. ICSH review of the measurement of the erythrocyte sedimentation rate. Int J Lab Hematol. 2011;33(2):125-132. doi:10.1111/j.1751-553X.2011.01302.x
- Kratz A, Plebani M, Peng M, Lee YK, McCafferty R, Machin SJ. ICSH recommendations for modified and alternate methods measuring the erythrocyte sedimentation rate. Int J Lab Hematol. 2017;39(5):448-457. doi:10.1111/ijlh.12693
Watch one
A repeat CBC confirms a hemoglobin of 18.6 g/dL, unchanged from a result 3 months ago. The patient has no history of dehydration, smoking, high altitude, or lung or heart disease. What is the next test?
- Confirm persistence: the repeat CBC matches the result from 3 months ago.
A persistent increase is confirmed against prior results before further testing is ordered.
- Review the history: no dehydration, smoking, altitude, or cardiopulmonary disease to explain a secondary cause.
Ruling out plasma-volume loss and hypoxia narrows the differential before a specific test is chosen.
- Order serum erythropoietin (EPO) as the next test.
Serum EPO separates a primary from a secondary process before molecular testing is ordered.
- A subnormal EPO result would support a primary process and would make JAK2 V617F testing the next step.
A subnormal EPO is what makes polycythemia vera plausible enough to test for.
Your turn
Use it
- A man, MRN 0392718, splenectomized 5 years ago after trauma, reports fatigue and joint pain.
- The emergency department orders a CBC with film, an ESR, and a sickle solubility screen.
- The film shows several red cells with small, clustered, dark granules.
- The ESR specimen arrives in a 9:1 sodium citrate coagulation tube.
- The sickle solubility screen returns positive.
The clue that settles this case is that none of the three findings can be reported on its own: the clustered granules need a Prussian blue stain before they are called iron, the ESR specimen's 9:1 ratio means the result cannot be trusted regardless of what it reads, and the positive sickle screen needs fractionation before trait or disease is named.
Results
- Choose an iron stain to confirm suspected Pappenheimer bodies
- Report a positive Hb S solubility screen without calling trait or disease
- Choose between a repeat count, EPO, and JAK2 V617F for a raised hemoglobin
- Recognize how citrate ratio, anemia, tube tilt, and temperature change a Westergren ESR
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